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Probable initial pulmonary lymphangioleiomyomatosis and mediastinal lymphangioleiomyoma

dc.contributor.authorPontes, M
dc.contributor.authorBarbosa, C
dc.contributor.authorCoelho, ML
dc.contributor.authorCarvalho, L
dc.date.accessioned2013-12-12T11:52:43Z
dc.date.available2013-12-12T11:52:43Z
dc.date.issued2013
dc.description.abstractA 68 year old woman was submitted to a mediastinal lymphangioleiomyoma resection found in a follow-up study of lower left lung resection due to bronchiectasis complicated by chylothorax. This led to a revaluation of the pulmonary specimen that revealed, in addition to inflammatory bronchiectasis, small spindle cell nodules in the lung parenchyma, similar to minute pulmonary meningothelial-like nodules, but with smooth muscle actin immunohistochemical positivity. The possibility of initial pulmonary development of lymphangioleiomyomatosis is discussed.por
dc.identifier.citationRev Port Pneumol. 2013: S0873-2159(13)00104-9.por
dc.identifier.urihttp://hdl.handle.net/10400.4/1599
dc.language.isoporpor
dc.peerreviewedyespor
dc.publisherSociedade Portuguesa de Pneumologiapor
dc.subjectLinfangioleiomiomatosepor
dc.subjectLinfangiomiomapor
dc.titleProbable initial pulmonary lymphangioleiomyomatosis and mediastinal lymphangioleiomyomapor
dc.title.alternativeLinfangioleiomiomatose pulmonar inicial provável e linfangioleiomioma mediastinalpor
dc.typejournal article
dspace.entity.typePublication
rcaap.rightsopenAccesspor
rcaap.typearticlepor

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