A propósito de um caso de espessamento cutâneo

Serra, S; Ambrósio, C; Salvador, MJ; Silva, J; Serra, D; Reis, JP; Malcata, AB

http://hdl.handle.net/10400.4/905

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Abstract(s)

The authors present a clinical case of a 79 years old female patient, with a progressive cutaneous thickening of the face, trunk and limbs, lasting for 6 years. She also presented exertional dyspnea and intermittent solid dysphagia. The laboratory study identified IgG KAPA monoclonal protein and antinuclear antibodies with a speckled pattern. The nailfold capillaroscopy was normal. A detailed physical examination together with cutaneous histopathology led to the diagnosis of Scleromyxedema, a rare cutaneous scleroderma like disease. The differential diagnosis of cutaneous sclerosis is discussed.