Pontes, MBarbosa, CCoelho, MLCarvalho, L2013-12-122013-12-122013Rev Port Pneumol. 2013: S0873-2159(13)00104-9.http://hdl.handle.net/10400.4/1599A 68 year old woman was submitted to a mediastinal lymphangioleiomyoma resection found in a follow-up study of lower left lung resection due to bronchiectasis complicated by chylothorax. This led to a revaluation of the pulmonary specimen that revealed, in addition to inflammatory bronchiectasis, small spindle cell nodules in the lung parenchyma, similar to minute pulmonary meningothelial-like nodules, but with smooth muscle actin immunohistochemical positivity. The possibility of initial pulmonary development of lymphangioleiomyomatosis is discussed.porLinfangioleiomiomatoseLinfangiomiomajournal article