Carvalho, SBarbosa, VSantos, NMachado, E2008-11-272008-11-272003AJNR Am J Neuroradiol. 2003 Oct;24(9):1916-8http://hdl.handle.net/10400.4/176We report a case of a 45-year-old woman known to have a familial form of blue rubber-bleb nevus syndrome (BRBNS). The patient developed severe occipital headaches and bilateral retroauricular bruits. Cerebral angiography showed a large dural arteriovenous fistula in the torcular region. Central nervous system involvement in BRBNS is not often reported, and most cases of BRBNS are sporadic.engNevo AzulSíndromes Neoplásicos HereditáriosAngiografia CerebralRessonância Magnéticajournal article