Publication
Bowel-associated dermatosis-arthritis syndrome in an adolescent with short bowel syndrome
| dc.contributor.author | Pereira, E | |
| dc.contributor.author | Estanqueiro, P | |
| dc.contributor.author | Almeida, S | |
| dc.contributor.author | Ferreira, R | |
| dc.contributor.author | Tellechea, O | |
| dc.contributor.author | Salgado, M | |
| dc.date.accessioned | 2016-07-08T11:58:52Z | |
| dc.date.available | 2016-07-08T11:58:52Z | |
| dc.date.issued | 2014-09 | |
| dc.description.abstract | Bowel-associated dermatosis-arthritis syndrome (BADAS) is a neutrophilic dermatosis, characterized by the occurrence of arthritis and skin lesions related to bowel disease with or without bowel bypass. We report an unusual case of BADAS in a 15-year-old white male with congenital aganglionosis of the colon and hypoganglionosis of the small intestine and multiple bowel surgeries in childhood complicated by short bowel syndrome. He presented with recurrent peripheral polyarthritis, tenosynovitis, and painful erythematous subcutaneous nodules located on the dorsolateral regions of the legs and on the dorsa of the feet. Histological examination disclosed a neutrophilic dermatosis confirming the diagnosis of BADAS.Although an uncommon disease, especially at pediatric age, it is important to evoke the diagnosis of BADAS in children and adolescents with bowel disease, because treatment options and prognosis are distinct from other rheumatologic conditions. | pt_PT |
| dc.identifier.citation | J Clin Rheumatol. 2014 Sep;20(6):322-4. | pt_PT |
| dc.identifier.doi | 10.1097/RHU.0000000000000137 | pt_PT |
| dc.identifier.uri | http://hdl.handle.net/10400.4/1940 | |
| dc.language.iso | eng | pt_PT |
| dc.peerreviewed | yes | pt_PT |
| dc.subject | Tenossinovite | pt_PT |
| dc.subject | Artrite | pt_PT |
| dc.subject | Adolescente | pt_PT |
| dc.subject | Doenças da Pele | pt_PT |
| dc.subject | Síndrome do Intestino Curto | pt_PT |
| dc.subject | Doença de Hirschsprung | pt_PT |
| dc.title | Bowel-associated dermatosis-arthritis syndrome in an adolescent with short bowel syndrome | pt_PT |
| dc.type | journal article | |
| dspace.entity.type | Publication | |
| oaire.citation.issue | 6 | pt_PT |
| oaire.citation.startPage | 322-4 | pt_PT |
| oaire.citation.title | Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases | pt_PT |
| oaire.citation.volume | 20 | pt_PT |
| rcaap.rights | openAccess | pt_PT |
| rcaap.type | article | pt_PT |